Primary Renal Perivascular Epithelioid Cell Tumor with CLTC::TFE3 Gene Fusion: A Rare Gene Fusion and Masquerading as Renal Cell Carcinoma
International Journal of Surgical Pathology
Published online on July 29, 2026
Abstract
International Journal of Surgical Pathology, Ahead of Print.
We report a primary perivascular epithelioid cell tumor (PEComa) of the kidney harboring a novelCLTC::TFE3gene fusion in a 51-year-old woman. The tumor was composed of high-grade epithelioid cells with clear to eosinophilic cytoplasm arranged in nested ...
We report a primary perivascular epithelioid cell tumor (PEComa) of the kidney harboring a novelCLTC::TFE3gene fusion in a 51-year-old woman. The tumor was composed of high-grade epithelioid cells with clear to eosinophilic cytoplasm arranged in nested ...