Fibroma-Like PEComa as an Early Indicator of Tuberous Sclerosis Complex: Confirmed With Strong GPNMB Expression and TSC2 Germline Mutation
International Journal of Surgical Pathology
Published online on January 07, 2026
Abstract
International Journal of Surgical Pathology, Ahead of Print.
Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms defined by co-expression of melanocytic and smooth muscle markers, with fibroma-like PEComa representing a novel and recently described subtype strongly associated with tuberous ...
Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms defined by co-expression of melanocytic and smooth muscle markers, with fibroma-like PEComa representing a novel and recently described subtype strongly associated with tuberous ...